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Porphyrin-binding effect of cholestyramine. Influence of chloroquine on the porphyrin metabolism.

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Summary Hereditary hemochromatosis HH is a common genetic disease in Tratamenfo, characterized by iron overload and resulting in damage of the liver and other organs.

Your feedback has been submitted successfully. Results of in vitro and in vivo studies. A unique dark effect of porphyrin. Plasma ferritin levels as a guide to the treatment of porphyria cutanea tarda by venesection. Discoid lupus erythematosus and porphyria cutanea tarda.

A population-based study of the clinical expression of the hemochromatosis gene. Survival and causes of death in cirrhotic and noncirrhotic patients with primary hemochromatosis.


Guidelines | European Federation of Associations of Patients with Haemochromatosis

A novel MHC class 1-like gene is mutated in patients with hereditary haemochromatosis. Dtsch Arch Klin Med.

Porphyria cutanea tarda during maintenance haemodialysis. Articular cartilage in the degenerative arthropathy of hemochromatosis.


Intratechal enzyme replacement therapy in a patient with mucopolysaccharidosis type I and symptomatic spinal cord compression. Haemophilia, hepatitis and porphyria. If your hospital, university, trust or other tgatamento provides access to Best Practice, log in via the appropriate link below:.

Mouse model for protoporphyria. How to cite this article. HFE genotypes and outcome after liver transplantation Hepatology ; The main factors limiting prognosis and patient wellbeing are identified. The development hemocro,atose prognosis of chronic intoxication by tetrachlorodibenzo-p-dioxin in men.

Treatment of inborn errors of metabolism

Alcoholic beverages in acute porphyria. Sassa S, Kappas A. Manual of metabolic paediatrics. Lim HW, Gigli I. Oxidation of uroporphyrinogens by hydroxyl radicals: How to cite this article.

J Hepatol ; Hemocromatise one of the access methods below or take a look at our subscribe or free trial options. An inherited enzymatic defect in porphyria cutanea tarda: A tratammento study of the results of phlebotomy therapy and low-dose chloroquine treatment in porphyria cutanea tarda. Biochemical diagnosis of the cutaneous porphyrias: Porphyria cutanea tarda in a dialyzed patient with hepatitis C virus infection: The treatment of porphyria cutanea tarda by venesection.


Porphyria cutanea tarda in association with human immunodeficiency virus infection: Activation of complement by nm light in serum from porphyria cutanea tarda. Tratamento a hemoctomatose prazo: Disrupted hepcidin regulation in HFE-associated haemochromatosis and liver as a regulator of body iron homeostasis.

Uroporphyrin I stimulation of collagen biosynthesis in human skin fibroblasts. Porphyria cutanea tarda, or the uroporphyrinogen decarboxylase deficiency diseases. Altomare G, Capella GL.